第54回日本小児循環器学会総会・学術集会

第54回日本小児循環器学会総会・学術集会

2018年7月5日〜7月7日パシフィコ横浜
日本小児循環器学会総会・学術集会
第54回日本小児循環器学会総会・学術集会

第54回日本小児循環器学会総会・学術集会

2018年7月5日〜7月7日パシフィコ横浜

[II-AEPCJS-01]How to assess the Tricuspid valve and RV function in CCTGA by CMR

Inga Voges(University Hospital Schleswig-Holstein, Campus Kiel, Department of Congenital Heart Disease and Paediatric Cardiology, Kiel, Germany)
Congenitally corrected Transposition of the great arteries (ccTGA) is a rare cardiac malformation characterized by the combination of discordant atrioventricular and ventriculo-arterial connections and is usually accompanied by other malformations such as ventricular septal defects, obstruction of the morphologically LV outflow tract and lesions of the tricuspid valve.
In patients with ccTGA the systemic right ventricle (RV) and its tricuspid valve are exposed to systemic arterial afterload and great concern exists about the ability of the anatomic RV to sustain the systemic circulation over the long term. Cardiovascular magnetic resonance imaging plays an important role in the evaluation of ccTGA patients during follow-up as it offers an accurate quantification of RV volumes and function as well as evaluation of the tricuspid valve.
In this presentation the various CMR methods for the detailed assessment of the systemic RV and the tricuspid valve are presented in the light of the current literature in ccTGA.