Session Details

[S8]シンポジウム8 小児急性脳症の到達点と将来展望

Fri. Jun 6, 2025 6:45 PM - 8:45 PM JST
Fri. Jun 6, 2025 9:45 AM - 11:45 AM UTC
第1会場
座長:阿部 裕一(国立成育医療研究センター神経内科) ,髙梨 潤一(東京女子医科大学八千代医療センター小児科)
本シンポジウムでは我が国の小児に好発する小児急性脳症の最新情報・到達点と今後解決すべき課題を共有することを目的とします。まず、第3回小児急性脳症全国疫学調査(令和2年4月から令和5年10 月)結果から、特にCOVID-19に伴う小児急性脳症の疫学変化を報告いただきます。小児急性脳症の疾患関連遺伝子解析、小児急性脳症レジストリ(FACEレジストリ)から得られた知見、COVID-19で増加が報告されたhemorrhagic shock and encephalopathy syndrome (HSES)、encephalopathy with acute fulminant cerebral edema (AFCE)に関する最新情報・課題をお伝えし、明日からの脳症診療に益することを目指します。

[S8-1]The third national survey on pediatric acute encephalopathy in Japan (April 2020 to October 2023)

Taku Omata (Department of Pediatrics, Tokyo Women’s Medical University Yachiyo Medical Center, Yachiyo, Japan)

[S8-2]Identification of Disease-Associated Genes in Acute Encephalopathy and Status Epilepticus Associated with Fever

Yamaguchi Hiroshi, Nagase Hiroaki (Department of Pediatrics, Kobe University Graduate School of Medicine, Hyogo, Japan)

[S8-3]Optimizing the treatment of acute encephalopathy: insights from the FACE registry

Masahiro Nishiyama1,2, Hiroaki Nagase2 (1.Department of Neurology, Hyogo Prefectural Kobe Children's Hospital, Kobe, Japan, 2.Department of Pediatrics, Kobe University Graduate School of Medicine, Kobe, Japan)

[S8-4]Clinical features of SARS-CoV-2-associated acute fulminant cerebral edema in Asia and Oceania

Mariko Kasai1, Hiroshi Sakuma1, Motomasa Suzuki2, Nanako Kawata3, Masahiro Nishiyama4, Jun-ichi Takanashi5 (1.Department of Brain and Neurosciences, Tokyo Metropolitan Institute of Medical Science, Tokyo, Japan, 2.Department of Pediatric Neurology, Aichi Children's Health and Medical Center, Obu, Japan, 3.Department of Neurology, Tokyo Metropolitan Children's Medical Center, Tokyo, Japan, 4.Department of Neurology, Hyogo Prefectural Kobe Children's Hospital, Kobe, Japan, 5.Department of Pediatrics and Pediatric Neurology, Tokyo Women's Medical University Yachiyo Medical Center, Chiba, Japan)

[S8-5]Pathophysiology of cerebral edema given the differentiation between HSES and ABS

Ichiro Kuki (Division of Pediatric Neurology and Neurolinguistics, Osaka City General Hospital)