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[O-22-2]Functions of the nigrostriatal system in PRNP-P102L variant Gerstman-Sträussler-Scheinker disease

Natsuki Ono1,2,3, Kohei Suzuyama2, Hiromu Minagawa3, Kiku Uwatoko3, Masaaki Yoshikawa2, Toshihiro Ide2, Miyuki Mitsuoka4, Kazuo Honda6, Tetsuyoshi Hirai5, Takateru Otsuka6, Keita Kai7, Hiroyuki Honda8, Tetsuyuki Kitamoto9,10, Hiroyuki Irie5, Motohiro Yukitake3, Haruki Koike2 (1.Department of Neurology, Imari Arita Kyoritsu Hospital, Japan, 2.Division of Neurology, Department of Internal Medicine, Faculty of Medicine, Saga University, Japan, 3.Department of Neurology, Kouhoukai Takagi Hospital, Japan, 4.Department of Radiology, Saga University Hospital, Japan, 5.Department of Radiology, Faculty of Medicine, Saga University, Japan, 6.Department of Radiology, Kouhoukai Takagi Hospital, Japan, 7.Department of Pathology, Saga University Hospital, Japan, 8.Neuropathology Center, NHO, Omuta Hospital, Japan, 9.Department of Neurological Science, Tohoku University School of Medicine, Japan, 10.department of clinical laboratory, National Center of Neurology and Psychiatry, Japan)

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