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[Pe-010-4]Opposing Effects of RNA-binding Proteins TDP-43 and FUS on DPR-mediated Neurodegeneration in SCA36

Tomoya Taminato1, Takeuchi Toshihide2, Toru Yamashita3, Yoshio Ikeda4, Koji Abe5, Yoshitaka Nagai1,2 (1.Dept Neurology, Kindai Univ Faculty of Med, Osaka, Japan, 2.Kindai University Life Science Research Institute, Japan, 3.Dept Neurology, Okayama Univ Grad Sch of Med, Okayama, Japan, 4.Dept Neurology, Gunma Univ Grad Sch of Med, Gunma, Japan, 5.Dept Neurology, National Center Neurol and Psychiatry, Tokyo, Japan)

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