Presentation Information
[StO-01-4]Deficiency of SSBP1-HSF1 Axis Leads to Disruption of Mitochondrial Proteostasis in Kii ALS/PDC
Chris Kato1,2, Satoru Morimoto1,2,3, Yuhko Kobayashi4, Yoshifumi Hirokawa3, Issei Kobayashi4, Terunori Sano5, Maho Morishima5,6, Masaki Takao5, Yuko Saito6, Mari Yoshida7, Shigeo Murayama6, Hideyuki Okano1, Yasumasa Kokubo8 (1.Keio Regenerative Medicine Research Center, Keio University, Japan, 2.Division of Neurodegenerative Disease Research, Tokyo Metropolitan Institute for Geriatrics and Gerontology, Japan, 3.Department of Oncologic Pathology, Mie University Graduate School of Medicine, Japan, 4.Center for Molecular Biology and Genetics, Mie University, Japan, 5.Department of Clinical Laboratory and Internal Medicine, National Center of Neurology and Psychiatry (NCNP), National Center Hospital, Japan, 6.Department of Neuropathology (the Brain Bank for Aging Reseach, Tokyo Metropolitan Institute for Geriatrics and Gerontology, Japan, 7.Institute for Medical Science of Aging, Aichi Medical University, Japan, 8.Kii ALS/PDC Research Centre, Mie University Graduate School of Regional Innovation Studies, Japan)