講演情報
[II-AHAJS-3]Adult Congenital Heart Disease and Heart Failure
○Curt Daniels (The Ohio State University Nationwide Children’s Hospital)
キーワード：
Adult Congenital Heart Disease、Heart Failure、Goal Directed Medical Therapies
Due to advances in surgical and medical congenital heart disease care, more than 90% of patients are expected to survive to adulthood, and as such, there are more adults than children living with congenital heart disease. However, long term survival is reduced for adults with congenital heart disease (ACHD), and heart failure is a major cause of morbidity and the leading cause of mortality. Compared to patients with acquired HF, the ACHD population with HF is unique and includes those with complex forms of CHD, systemic right ventricles, and single ventricle anatomy with Fontan palliation. Additionally, there is a lack of data and lack of evidence to support most medical therapies in ACHD HF and patients are less likely to be treated with advanced HF therapies, including durable mechanical circulatory support or heart transplant. However, there is hope for improving outcomes. New information and technology, advanced education and training, programmatic accreditation, and more recent data have emerged to improve our understanding and care for the ACHD HF population including recent studies with medical therapies, new training guidelines for ACHD HF, utilizing ambulatory hemodynamic monitors, and risk scoring for advanced therapies and transplant listing.